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Date: Tue Jan 28 2025
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lymphoproliferative syndrome
DOID:0060704
Summary
Associated Genes
Associated Alleles
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Disease
lymphoproliferative syndrome
Definition
A primary immunodeficiency disease characterized by immune dysregulation typically after viral infection, usually associated with Epstein-Barr viral infection.
[1]
[2]
Synonyms
Combined immunodeficiency due to ITK deficiency
Cross References
MIM:PS308240
ORDO:538963
Parent Terms
primary immunodeficiency disease
Child Terms
Castleman disease
lymphomatoid granulomatosis
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ZFIN
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