Contributes to metalloendopeptidase activity. Involved in proteolysis. Part of mitochondrial processing peptidase complex. Human ortholog(s) of this gene implicated in autosomal recessive spinocerebellar ataxia 2. Orthologous to human PMPCA (peptidase, mitochondrial processing subunit alpha).
WB Description
Contributes to metalloendopeptidase activity. Involved in proteolysis. Part of mitochondrial processing peptidase complex. Human ortholog(s) of this gene implicated in autosomal recessive spinocerebellar ataxia 2. Is an ortholog of human PMPCA (peptidase, mitochondrial processing subunit alpha).