Version: 8.0.0Date: Tue Jan 28 2025
Gene Biological Process: establishment of localization Cellular Component: mitochondrial inner membrane
Dmd
(Mus musculus)Gene
Name: dystrophin, muscular dystrophy
Synonyms: mdx, X-linked muscular dystrophy, Duchenne muscular dystrophy, Dp71, DNADMD1, pke, pyruvate kinase expression, Dp427, dys
Source: MGI:94909
Biotype: protein coding gene
Apex2
(Mus musculus)Gene
Name: apurinic/apyrimidinic endonuclease 2
Synonyms: C430040P13Rik, RIKEN cDNA C430040P13 gene, Ape2
Source: MGI:1924872
Biotype: protein coding gene
UQCC6
(Homo sapiens)Gene
Name: ubiquinol-cytochrome c reductase complex assembly factor 6
Synonyms: BR, ubiquinol-cytochrome-c reductase complex assembly factor 6, hypothetical protein LOC728568, BRAWNIN, C12orf73, DKFZp547P055, chromosome 12 open reading frame 73, FLJ13975, uncharacterized protein C12orf73
Source: HGNC:34450
Biotype: protein coding gene
Adck1
(Mus musculus)Gene
Name: aarF domain containing kinase 1
Synonyms: 2610005A10Rik, RIKEN cDNA 2610005A10 gene
Source: MGI:1919363
Biotype: protein coding gene
Sdha
(Mus musculus)Gene
Name: succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
Synonyms: C81073, expressed sequence C81073, RIKEN cDNA 2310034D06 gene, 2310034D06Rik, SDHF, FP, SDH2
Source: MGI:1914195
Biotype: protein coding gene
CYCS
(Homo sapiens)Gene
Name: cytochrome c, somatic
Synonyms: THC4, HCS, cytochrome c, CYC
Source: HGNC:19986
Biotype: protein coding gene
CAT2
(Saccharomyces cerevisiae)Gene
Name: Carnitine AcetylTransferase
Synonyms: YML042W, YCAT
Source: SGD:S000004506
Biotype: protein coding gene
Aldh18a1
(Mus musculus)Gene
Name: aldehyde dehydrogenase 18 family, member A1
Synonyms: 2810433K04Rik, pyrroline-5-carboxylate synthetase (glutamate gamma-semialdehyde synthetase), expressed sequence AI429789, RIKEN cDNA 2810433K04 gene, Pycs, AI429789
Source: MGI:1888908
Biotype: protein coding gene
Pdk4
(Mus musculus)Gene
Name: pyruvate dehydrogenase kinase, isoenzyme 4
Synonyms: expressed sequence AV005916, AV005916
Source: MGI:1351481
Biotype: protein coding gene
PISD
(Homo sapiens)Gene
Name: phosphatidylserine decarboxylase
Synonyms: PSD, DKFZp566G2246, phosphatidylserine decarboxylase proenzyme, mitochondrial, LIBF, DJ858B16, PSSC, PSDC, dJ858B16.2, phosphatidylserine decarboxylase proenzyme
Source: HGNC:8999
Biotype: protein coding gene
CYP1A1
(Homo sapiens)Gene
Name: cytochrome P450 family 1 subfamily A member 1
Synonyms: cytochrome P450, family 1, subfamily A, polypeptide 1, AHH, cytochrome P450 1A1, cytochrome P450, subfamily I (aromatic compound-inducible), polypeptide 1, CYP1, P1-450, P450DX, P450-C, xenobiotic monooxygenase, flavoprotein-linked monooxygenase, cytochrome P450-C, CP11, cytochrome P450-P1, cytochrome P1-450, dioxin-inducible, aryl hydrocarbon hydroxylase, cytochrome P450 form 6, AHRR, hydroperoxy icosatetraenoate dehydratase, CYPIA1
Source: HGNC:2595
Biotype: protein coding gene
CYP11B1
(Homo sapiens)Gene
Name: cytochrome P450 family 11 subfamily B member 1
Synonyms: cytochrome P450C11, cytochrome P450, subfamily XIB (steroid 11-beta-hydroxylase), polypeptide 1, DKFZp686B05283, steroid 11-beta-hydroxylase, CYP11B1, FHI, cytochrome P450 11B1, mitochondrial, CYPXIB1, steroid 11-beta-monooxygenase, CPN1, FLJ36771, cytochrome P450, family 11, subfamily B, polypeptide 1, P450C11, cytochrome p450 XIB1, CYP11B, cytochrome P-450c11, steroid 11-beta-hydroxylase
Source: HGNC:2591
Biotype: protein coding gene
FECH
(Homo sapiens)Gene
Name: ferrochelatase
Synonyms: protoheme ferro-lyase, ferrochelatase, mitochondrial, heme synthetase, EPP, heme synthase, FCE, EPP1, protoporphyria
Source: HGNC:3647
Biotype: protein coding gene
Suclg1
(Mus musculus)Gene
Name: succinate-CoA ligase, GDP-forming, alpha subunit
Synonyms: Sucla1, RIKEN cDNA 1500000I01 gene, 1500000I01Rik
Source: MGI:1927234
Biotype: protein coding gene
Hmgcs2
(Mus musculus)Gene
Name: 3-hydroxy-3-methylglutaryl-Coenzyme A synthase 2
Synonyms: Mt3h3mg, Hmgcs1, mHS
Source: MGI:101939
Biotype: protein coding gene
Cpt2
(Mus musculus)Gene
Name: carnitine palmitoyltransferase 2
Synonyms: CPTII, expressed sequence AI323697, CPT II, AI323697
Source: MGI:109176
Biotype: protein coding gene
Cps1
(Mus musculus)Gene
Name: carbamoyl-phosphate synthetase 1
Synonyms: D1Ucla3, CPSase I, CPS, 4732433M03Rik, cps, RIKEN cDNA 4732433M03 gene, DNA segment, Chr 1, University of California at Los Angeles 3, cps-1
Source: MGI:891996
Biotype: protein coding gene
Glud1
(Mus musculus)Gene
Name: glutamate dehydrogenase 1
Synonyms: Gdh-X, Gludl, Ac2-281, anonymous DNA segment, Chr 14, MRG-2, Glud, Gdh1, expressed sequence AI118167, glutamate dehydrogenase like sequence, Gludeha, AI118167
Source: MGI:95753
Biotype: protein coding gene
Otc
(Mus musculus)Gene
Name: ornithine transcarbamylase
Synonyms: sparse fur, Sf, AI265390, spf, expressed sequence AI265390, Sparse-fur
Source: MGI:97448
Biotype: protein coding gene
Cox15
(Mus musculus)Gene
Name: cytochrome c oxidase assembly protein 15
Synonyms: 2900026G05Rik, RIKEN cDNA 2900026G05 gene
Source: MGI:1920112
Biotype: protein coding gene
Sdhd
(Mus musculus)Gene
Name: succinate dehydrogenase complex, subunit D, integral membrane protein
Synonyms: CII-4, expressed sequence C78570, cybS, QPs3, C78570, 3110001M13Rik, RIKEN cDNA 3110001M13 gene
Source: MGI:1914175
Biotype: protein coding gene
GUT2
(Saccharomyces cerevisiae)Gene
Name: Glycerol UTilization
Synonyms: YIL155C
Source: SGD:S000001417
Biotype: protein coding gene
Hadh
(Mus musculus)Gene
Name: hydroxyacyl-Coenzyme A dehydrogenase
Synonyms: AW742602, expressed sequence AW742602, expressed sequence AA409008, hydroxylacyl-Coenzyme A dehydrogenase-dehydrogenase, hydroxylacyl-Coenzyme A dehydrogenase, AA409008, Schad, L-3-hydroxyacyl-Coenzyme A dehydrogenase, short chain, expressed sequence AU019341, Hadhsc, AU019341
Source: MGI:96009
Biotype: protein coding gene
PHB1
(Homo sapiens)Gene
Name: prohibitin 1
Synonyms: BAP32, HEL-S-54e, epididymis luminal protein 215, PHB, HEL-215, epididymis secretory sperm binding protein Li 54e, prohibitin
Source: HGNC:8912
Biotype: protein coding gene
UQCRC2
(Homo sapiens)Gene
Name: ubiquinol-cytochrome c reductase core protein 2
Synonyms: MC3DN5, core protein II, UQCR2, QCR2, cytochrome b-c1 complex subunit 2, mitochondrial, complex III subunit 2, cytochrome bc-1 complex core protein II, ubiquinol-cytochrome c reductase core protein II, ubiquinol-cytochrome-c reductase complex core protein 2
Source: HGNC:12586
Biotype: protein coding gene
Mccc1
(Mus musculus)Gene
Name: methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)
Synonyms: MCCA, expressed sequence R75106, RIKEN cDNA 1810045E08 gene, 1810045E08Rik, R75106, MCCalpha, 2310058B18Rik, RIKEN cDNA 2310058B18 gene
Source: MGI:1919289
Biotype: protein coding gene
Mtfp1
(Mus musculus)Gene
Name: mitochondrial fission process 1
Synonyms: RIKEN cDNA 1700020C11 gene, Mtp18, 2610507A21Rik, 1700020C11Rik, expressed sequence AV005788, AV005788, RIKEN cDNA 2610507A21 gene
Source: MGI:1916686
Biotype: protein coding gene
Mfn1
(Mus musculus)Gene
Name: mitofusin 1
Synonyms: DNA segment, Chr 3, ERATO Doi 265, expressed, D3Ertd265e, RIKEN cDNA 6330416C07 gene, 2310002F04Rik, 6330416C07Rik, HR2, RIKEN cDNA 2310002F04 gene, Fzo1b
Source: MGI:1914664
Biotype: protein coding gene
UQCRQ
(Homo sapiens)Gene
Name: ubiquinol-cytochrome c reductase complex III subunit VII
Synonyms: complex III subunit 8, MC3DN4, QPC, ubiquinol-cytochrome c reductase complex 9.5 kDa protein, cytochrome b-c1 complex subunit 8, ubiquinol-cytochrome c reductase, complex III subunit VII, low molecular mass ubiquinone-binding protein (9.5kD), ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa, ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C, QP-C, complex III subunit VIII, QCR8, UQCR7
Source: HGNC:29594
Biotype: protein coding gene
ADCK1
(Homo sapiens)Gene
Name: aarF domain containing kinase 1
Synonyms: uncharacterized aarF domain-containing protein kinase 1, FLJ39600, MCP2, aarF domain-containing protein kinase 1
Source: HGNC:19038
Biotype: protein coding gene
Mpst
(Mus musculus)Gene
Name: mercaptopyruvate sulfurtransferase
Synonyms: 3MST, Mst
Source: MGI:2179733
Biotype: protein coding gene
Pcx
(Mus musculus)Gene
Name: pyruvate carboxylase
Synonyms: Pc
Source: MGI:97520
Biotype: protein coding gene
Hmgcl
(Mus musculus)Gene
Name: 3-hydroxy-3-methylglutaryl-Coenzyme A lyase
Synonyms: AW476067, expressed sequence AW476067
Source: MGI:96158
Biotype: protein coding gene
mt:CoII
(Drosophila melanogaster)Gene
Name: mitochondrial Cytochrome c oxidase subunit II
Synonyms: CO II, CO2, cox2, cytochrome c oxidase, CoII, mt:co2, COII, Cytochrome c oxidase I, mt-CO2, COX2, COXII, cytochrome c, COI, CG34069, II, Co-II, cytochrome oxidase II, Cox2, mt:coII, CytoCox, CO, COX, Cytochrome c oxidase subunit II, CcO subunit II, mt:Cox2, cytochrome c oxidase subunit II, mt:COII, MT-CO2, dMtCOXII, mt COII
Source: FB:FBgn0013675
Biotype: protein coding gene
Kmo
(Mus musculus)Gene
Name: kynurenine 3-monooxygenase
Synonyms: expressed sequence AI046660, kynurenine 3-hydroxylase, AI046660
Source: MGI:2138151
Biotype: protein coding gene
Hsd3b5
(Mus musculus)Gene
Name: hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 5
Synonyms: Hsd3b, Hsd1, 3(beta)HSDV, RATHSDI
Source: MGI:104645
Biotype: protein coding gene
Fech
(Mus musculus)Gene
Name: ferrochelatase
Synonyms: expressed sequence AI894116, AI894116, fch, Fcl
Source: MGI:95513
Biotype: protein coding gene
Mrpl40
(Mus musculus)Gene
Name: mitochondrial ribosomal protein L40
Synonyms: Nlvcf, nuclear localization signal protein absent in velo-cardio-facial patients
Source: MGI:1332635
Biotype: protein coding gene
Cox4i1
(Mus musculus)Gene
Name: cytochrome c oxidase subunit 4I1
Synonyms: cytochrome c oxidase, subunit IVa, Cox4, cytochrome c oxidase, subunit IV, COXIV, AL024441, expressed sequence AL024441, Cox4a, cytochrome C oxidase, subunit IV
Source: MGI:88473
Biotype: protein coding gene
SHE9
(Saccharomyces cerevisiae)Gene
Name: Sensitivity to High Expression
Synonyms: MDM33, YDR393W
Source: SGD:S000002801
Biotype: protein coding gene
Gpx4
(Mus musculus)Gene
Name: glutathione peroxidase 4
Synonyms: 1700027O09Rik, mtPHGPx, snGPx, snGpx, sperm nuclei glutathione peroxidase, gpx-4, phospholipid hydroperoxide glutathione peroxidase, Gshpx-4, PHGPx, Phgpx
Source: MGI:104767
Biotype: protein coding gene
Cox5a
(Mus musculus)Gene
Name: cytochrome c oxidase subunit 5A
Synonyms: expressed sequence AA959768, CcOX, AA959768
Source: MGI:88474
Biotype: protein coding gene
PTPN1
(Homo sapiens)Gene
Name: protein tyrosine phosphatase non-receptor type 1
Synonyms: protein-tyrosine phosphatase 1B, protein tyrosine phosphatase 1B, PTP1B, protein tyrosine phosphatase, placental, tyrosine-protein phosphatase non-receptor type 1
Source: HGNC:9642
Biotype: protein coding gene
mev-1
(Caenorhabditis elegans)Gene
Name: abnormal MEthyl Viologen sensitivity 1
Synonyms: cyt-1, CELE_T07C4.7, T07C4.7, sdhc-1
Source: WB:WBGene00003225
Biotype: protein coding gene
PHB1
(Saccharomyces cerevisiae)Gene
Name: ProHiBitin
Synonyms: YGR132C
Source: SGD:S000003364
Biotype: protein coding gene
Cyp11a1
(Mus musculus)Gene
Name: cytochrome P450, family 11, subfamily a, polypeptide 1
Synonyms: Scc, D9Ertd411e, P450(scc), P450scc, Cypxia1, DNA segment, Chr 9, ERATO Doi 411, expressed, Cyp11a, cholesterol side chain cleavage, cscc
Source: MGI:88582
Biotype: protein coding gene
Tymp
(Rattus norvegicus)Gene
Name: thymidine phosphorylase
Synonyms: LOC315219, tdRPase, endothelial cell growth factor 1 (platelet-derived), TP, Ecgf1, MGC112734, MGC108801
Source: RGD:1305756
Biotype: protein coding gene
TAFAZZIN
(Homo sapiens)Gene
Name: tafazzin, phospholipid-lysophospholipid transacylase
Synonyms: BTHS, Taz1, EFE, G4.5, transcriptional coactivator with PDZ-binding motif, XAP-2, CMD3A, TAZ, FLJ27390, LVNCX, EFE2
Source: HGNC:11577
Biotype: protein coding gene
Acadvl
(Mus musculus)Gene
Name: acyl-Coenzyme A dehydrogenase, very long chain
Synonyms: VLCAD
Source: MGI:895149
Biotype: protein coding gene
Ldhb
(Rattus norvegicus)Gene
Name: lactate dehydrogenase B
Synonyms: LDH-H, Ldh2, Lactate dehydrogenease B, L-lactate dehydrogenase B, LDH heart subunit, L-lactate dehydrogenase B chain, LDH-B
Source: RGD:2997
Biotype: protein coding gene