Version: 8.0.0Date: Tue Jan 28 2025
Gene Biological Process: glycoprotein catabolic process
IDUA
(Homo sapiens)Gene
Name: alpha-L-iduronidase
Synonyms: MPS1, iduronidase, alpha-L-, iduronidase alpha-L-, IDA, MPSI, mucopolysaccharidosis type I
Source: HGNC:5391
Biotype: protein coding gene
FBXO6
(Homo sapiens)Gene
Name: F-box protein 6
Synonyms: Fbx6b, F-box protein that recognizes sugar chains 2, FBG2, F-box/G-domain protein 2, F-box protein FBG2, FBX6, F-box protein Fbx6, FBS2, F-box only protein 6
Source: HGNC:13585
Biotype: protein coding gene
NGLY1
(Homo sapiens)Gene
Name: N-glycanase 1
Synonyms: FLJ12409, PNG-1, peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase, FLJ11005, PNGase, hPNGase, CDDG, CDG1V, PNG1, peptide:N-glycanase
Source: HGNC:17646
Biotype: protein coding gene
STT3B
(Homo sapiens)Gene
Name: STT3 oligosaccharyltransferase complex catalytic subunit B
Synonyms: STT3, subunit of the oligosaccharyltransferase complex, homolog B, dolichyl-diphosphooligosaccharide protein glycotransferase, homolog of yeast STT3, source of immunodominant MHC associated peptides, FLJ90106, dolichyl-diphosphooligosaccharide--protein glycosyltransferase subunit STT3B, STT3B, catalytic subunit of the oligosaccharyltransferase complex, STT3-B, STT3B, subunit of the oligosaccharyltransferase complex (catalytic), CDG1X, SIMP, source of immunodominant MHC-associated peptides homolog, oligosaccharyl transferase subunit STT3B
Source: HGNC:30611
Biotype: protein coding gene
MAN1A1
(Homo sapiens)Gene
Name: mannosidase alpha class 1A member 1
Synonyms: HUMM9, HUMM3, Man9-mannosidase, man(9)-alpha-mannosidase, mannosyl-oligosaccharide 1,2-alpha-mannosidase IA, mannosidase, alpha, class 1A, member 1, MAN9, processing alpha-1,2-mannosidase IA, alpha-1,2-mannosidase IA
Source: HGNC:6821
Biotype: protein coding gene
PDI1
(Saccharomyces cerevisiae)Gene
Name: Protein Disulfide Isomerase
Synonyms: YCL043C, MFP1, TRG1
Source: SGD:S000000548
Biotype: protein coding gene
MANBA
(Homo sapiens)Gene
Name: mannosidase beta
Synonyms: mannanase, lysosomal beta A mannosidase, mannase, beta-mannosidase A, MANB1, beta-mannosidase, mannosidase, beta A, lysosomal
Source: HGNC:6831
Biotype: protein coding gene
BTK
(Homo sapiens)Gene
Name: Bruton tyrosine kinase
Synonyms: MGC126261, B-cell progenitor kinase, tyrosine-protein kinase BTK, MGC126262, truncated Bruton agammaglobulinemia tyrosine kinase, tyrosine-protein kinase BTK isoform (lacking exon 14), dominant-negative kinase-deficient Brutons tyrosine kinase, XLA, Bruton's tyrosine kinase, Bruton agammaglobulinemia tyrosine kinase, PSCTK1, IMD1, AT, AGMX1, agammaglobulinaemia tyrosine kinase, ATK, tyrosine-protein kinase BTK isoform (lacking exon 13 to 17), BPK, IGHD3
Source: HGNC:1133
Biotype: protein coding gene
IDS
(Homo sapiens)Gene
Name: iduronate 2-sulfatase
Synonyms: idursulfase, iduronate 2-sulfatase 42 kDa chain, SIDS, alpha-L-iduronate sulfate sulfatase, MPS2, iduronate 2-sulfatase 14 kDa chain, ID2S
Source: HGNC:5389
Biotype: protein coding gene
Pngl
(Drosophila melanogaster)Gene
Name: PNGase-like
Synonyms: Ngly1, CG7865, ngly1, dNGLY1, pngl, NGLY1, PNGase, png1, Png1
Source: FB:FBgn0033050
Biotype: protein coding gene
CTSL
(Homo sapiens)Gene
Name: cathepsin L
Synonyms: CTSL1, procathepsin L, MEP, CATL, FLJ31037, cathepsin L1, major excreted protein
Source: HGNC:2537
Biotype: protein coding gene
C14B1.3
(Caenorhabditis elegans)Gene
Name: F-box domain-containing protein
Synonyms: CELE_C14B1.3
Source: WB:WBGene00007574
Biotype: protein coding gene
ngly1
(Danio rerio)Gene
Name: N-glycanase 1
Synonyms: zgc:110561, im:6895151
Source: ZFIN:ZDB-GENE-050522-535
Biotype: protein coding gene
Mmp12
(Mus musculus)Gene
Name: matrix metallopeptidase 12
Synonyms: MMP12, Mmel, expressed sequence AV378681, Mme, macrophage metalloelastase, macrophage elastase, AV378681
Source: MGI:97005
Biotype: protein coding gene
MNS1
(Saccharomyces cerevisiae)Gene
Name: Not Available
Synonyms: YJR131W
Source: SGD:S000003892
Biotype: protein coding gene
Sgsh
(Drosophila melanogaster)Gene
Name: N-sulfoglucosamine sulfohydrolase
Synonyms: CG14291, SGSH
Source: FB:FBgn0038660
Biotype: protein coding gene
Hpse
(Mus musculus)Gene
Name: heparanase
Synonyms: Hep, Hpa
Source: MGI:1343124
Biotype: protein coding gene
Fbxo6
(Mus musculus)Gene
Name: F-box protein 6
Synonyms: Fbx6b, expressed sequence AA408845, AA408845, Fbg2, FBG2, Fbs2, F-box protein 6b, Fbxo6b
Source: MGI:1354743
Biotype: protein coding gene
Cela1
(Mus musculus)Gene
Name: chymotrypsin-like elastase family, member 1
Synonyms: elastase 1 (structural or pseudogene), Ela-1, RATELAI1, elastase 1, pancreatic, 1810009A17Rik, PC-TsF, 1810062B19Rik, Ela1, RIKEN cDNA 1810009A17 gene, RIKEN cDNA 1810062B19 gene, ELAI1
Source: MGI:95314
Biotype: protein coding gene
Ids
(Mus musculus)Gene
Name: iduronate 2-sulfatase
Synonyms: AW214631, expressed sequence AW214631
Source: MGI:96417
Biotype: protein coding gene
EDEM1
(Homo sapiens)Gene
Name: ER degradation enhancing alpha-mannosidase like protein 1
Synonyms: KIAA0212, EDEM, ER degradation enhancing alpha mannosidase-like, ER degradation-enhancing alpha-mannosidase-like 1, FLJ51560, ER degradation enhancer, mannosidase alpha-like 1, ER degradation-enhancing alpha-mannosidase-like protein 1, FLJ51559
Source: HGNC:18967
Biotype: protein coding gene
SGSH
(Homo sapiens)Gene
Name: N-sulfoglucosamine sulfohydrolase
Synonyms: mucopolysaccharidosis type IIIA, N-sulphoglucosamine sulphohydrolase, sulphamidase, HSS, MPS3A, SFMD, heparan sulfate sulfatase, sulfoglucosamine sulfamidase
Source: HGNC:10818
Biotype: protein coding gene
png-1
(Caenorhabditis elegans)Gene
Name: PNG (Peptide:N-Glycanase) homolog 1
Synonyms: bam-1, F56G4.5, CELE_F56G4.5
Source: WB:WBGene00010160
Biotype: protein coding gene
Edem1
(Drosophila melanogaster)Gene
Name: ER degradation enhancer, mannosidase alpha-like 1
Synonyms: Edem1, EG.86E4.2, edem1, EDEM1, dEDEM1, DM-pI, CG3810, EG:86E4.2
Source: FB:FBgn0023511
Biotype: protein coding gene
FBXO2
(Homo sapiens)Gene
Name: F-box protein 2
Synonyms: F-box only protein 2, OCP1, NFB42, FBX2, FBG1, F-box gene 1, organ of Corti protein 1, Fbs1, neural f box protein nfb42
Source: HGNC:13581
Biotype: protein coding gene
Glb1
(Mus musculus)Gene
Name: galactosidase, beta 1
Synonyms: Bge, Bgl, RIKEN cDNA C130097A14 gene, beta-galactosidase electrophoretic, Bgl-e, Bgt, beta-galactosidase complex, Bgs, beta-galactosidase temporal, beta-galactosidase systemic regulator, C130097A14Rik, expressed sequence AW125515, AW125515, Bgl-t, Bgl-s
Source: MGI:88151
Biotype: protein coding gene
Gusb
(Mus musculus)Gene
Name: glucuronidase, beta
Synonyms: beta-glucuronidase temporal, Gus, AI747421, Gur, beta-glucuronidase systemic regulator, g, Gut, beta-glucuronidase regulator, Ac2-223, expressed sequence AI747421, adipose storage deficiency, Gus-u, asd, Gus-t, Gus-s, Gus-r, beta-glucuronidase structural
Source: MGI:95872
Biotype: protein coding gene
Btk
(Mus musculus)Gene
Name: Bruton agammaglobulinemia tyrosine kinase
Synonyms: xid, X-linked immune deficiency, AI528679, Bruton's tyrosine kinase, expressed sequence AI528679
Source: MGI:88216
Biotype: protein coding gene
OGA
(Homo sapiens)Gene
Name: O-GlcNAcase
Synonyms: MGEA5, bifunctional protein NCOAT, FLJ23355, NCOAT, MEA5, FLJ11229, beta-N-acetylglucosaminidase, N-acetyl-beta-D-glucosaminidase, hyaluronidase in meningioma, meningioma expressed antigen 5 (hyaluronidase), nuclear cytoplasmic O-GlcNAcase and acetyltransferase, KIAA0679, beta-hexosaminidase, beta-N-acetylhexosaminidase, meningioma-expressed antigen 5, N-acetyl-beta-glucosaminidase
Source: HGNC:7056
Biotype: protein coding gene
Ctsl
(Mus musculus)Gene
Name: cathepsin L
Synonyms: 1190035F06Rik, Ctsl1, nackt, CATHL, RIKEN cDNA 1190035F06 gene, nkt, furless, MEP, CatL, fs, major excreted protein, Cat L
Source: MGI:88564
Biotype: protein coding gene
Manba
(Mus musculus)Gene
Name: mannosidase, beta A, lysosomal
Synonyms: RIKEN cDNA 2410030O07 gene, beta-mannosidase activity, liver, kidney, Bmn, RIKEN cDNA B930014J03 gene, B930014J03Rik, 2410030O07Rik
Source: MGI:88175
Biotype: protein coding gene
Edem1
(Mus musculus)Gene
Name: ER degradation enhancer, mannosidase alpha-like 1
Synonyms: RGD1563633, mKIAA0212, A130059K23Rik, RIKEN cDNA A130059K23 gene
Source: MGI:2180139
Biotype: protein coding gene
edem3
(Danio rerio)Gene
Name: ER degradation enhancer, mannosidase alpha-like 3
Synonyms: Not Available
Source: ZFIN:ZDB-GENE-070801-5
Biotype: protein coding gene
sgsh
(Danio rerio)Gene
Name: N-sulfoglucosamine sulfohydrolase (sulfamidase)
Synonyms: wu:fe14h11
Source: ZFIN:ZDB-GENE-030131-4958
Biotype: protein coding gene
Man1b1
(Mus musculus)Gene
Name: mannosidase, alpha, class 1B, member 1
Synonyms: ERMan1, E430019H13Rik, RGD1563595, gene model 108, (NCBI), MANA-ER, Gm108, LOC227619, RIKEN cDNA E430019H13 gene
Source: MGI:2684954
Biotype: protein coding gene
Fbxo6
(Rattus norvegicus)Gene
Name: F-box protein 6
Synonyms: F-box protein that recognizes sugar chains 2, F-box only protein 6b, F-box only protein 6 b, Fbg2, F-box/G-domain protein 2, F-box only protein 6, Fbxo6b
Source: RGD:620418
Biotype: protein coding gene
Edem2
(Mus musculus)Gene
Name: ER degradation enhancer, mannosidase alpha-like 2
Synonyms: expressed sequence AI327354, 9530090G24Rik, RIKEN cDNA 9530090G24 gene, AI327354, RGD1303074
Source: MGI:1915540
Biotype: protein coding gene
FBXO27
(Homo sapiens)Gene
Name: F-box protein 27
Synonyms: F-box/G-domain protein 5, F-box only protein 27, Fbx27, FBG5, F-box protein FBG5
Source: HGNC:18753
Biotype: protein coding gene
Ngly1
(Rattus norvegicus)Gene
Name: N-glycanase 1
Synonyms: LOC100909559, uncharacterized LOC100909559, LOC361014, N-glycanase 1 (predicted), peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase, Ngly1_predicted, similar to peptide N-glycanase, LOC289935, PNGase, peptide:N-glycanase
Source: RGD:1308518
Biotype: protein coding gene
Neu4
(Mus musculus)Gene
Name: sialidase 4
Synonyms: Not Available
Source: MGI:2661364
Biotype: protein coding gene
GPC1
(Homo sapiens)Gene
Name: glypican 1
Synonyms: FLJ38078, glypican-1, glypican proteoglycan 1, glypican
Source: HGNC:4449
Biotype: protein coding gene
Man1a
(Mus musculus)Gene
Name: mannosidase 1, alpha
Synonyms: Aa2-166, PCR1, mannosyl-oligosaccharide alpha-1,2-mannosidase
Source: MGI:104677
Biotype: protein coding gene
Idua
(Mus musculus)Gene
Name: iduronidase, alpha-L
Synonyms: Not Available
Source: MGI:96418
Biotype: protein coding gene
Adamts12
(Rattus norvegicus)Gene
Name: ADAM metallopeptidase with thrombospondin type 1 motif, 12
Synonyms: A disintegrin and metalloproteinase with thrombospondin motifs 12, a disintegrin-like and metalloprotease (reprolysin type) with thrombospondin type 1 motif, 12, LOC294809, a disintegrin-like and metallopeptidase (reprolysin type) with thrombospondin type 1 motif, 12
Source: RGD:1307323
Biotype: protein coding gene
Naglu
(Mus musculus)Gene
Name: alpha-N-acetylglucosaminidase (Sanfilippo disease IIIB)
Synonyms: RGD1564228
Source: MGI:1351641
Biotype: protein coding gene
YOS9
(Saccharomyces cerevisiae)Gene
Name: Yeast OS-9 homolog
Synonyms: YDR057W
Source: SGD:S000002464
Biotype: protein coding gene
NAGLU
(Homo sapiens)Gene
Name: N-acetyl-alpha-glucosaminidase
Synonyms: NAG, UFHSD, testicular tissue protein Li 18, alpha-N-acetylglucosaminidase, CMT2V, N-acetylglucosaminidase, alpha, MPS-IIIB, MPS3B
Source: HGNC:7632
Biotype: protein coding gene
fbxo44.5
(Danio rerio)Gene
Name: F-box protein 44, tandem duplicate 5
Synonyms: zgc:100832
Source: ZFIN:ZDB-GENE-040801-53
Biotype: protein coding gene
GUSB
(Homo sapiens)Gene
Name: glucuronidase beta
Synonyms: FLJ39445, MPS7, BG, beta-glucuronidase, beta-G1, beta-D-glucuronidase, glucuronidase, beta
Source: HGNC:4696
Biotype: protein coding gene
C33G3.4
(Caenorhabditis elegans)Gene
Name: Probable beta-mannosidase
Synonyms: CELE_C33G3.4
Source: WB:WBGene00007904
Biotype: protein coding gene