Version: 8.0.0Date: Tue Jan 28 2025
Gene Molecular Function: mitochondrial ribosome binding
C1QBP
(Homo sapiens)Gene
Name: complement C1q binding protein
Synonyms: SF2p32, GC1QBP, splicing factor SF2-associated protein, gC1Q-R, COXPD33, p32, C1q globular domain-binding protein, complement component 1 Q subcomponent-binding protein, mitochondrial, glycoprotein gC1qBP, p33, ASF/SF2-associated protein p32, mitochondrial matrix protein p32, hyaluronan-binding protein 1, SF2AP32, gC1qR, HABP1
Source: HGNC:1243
Biotype: protein coding gene
TACO1
(Homo sapiens)Gene
Name: translational activator of cytochrome c oxidase I
Synonyms: clone HQ0477 PRO0477p, CCDC44, translational activator of COX I, translational activator of mitochondrially encoded cytochrome c oxidase I, coiled-coil domain-containing protein 44, MC4DN8, translational activator of cytochrome c oxidase 1
Source: HGNC:24316
Biotype: protein coding gene
OXA1L
(Homo sapiens)Gene
Name: OXA1L mitochondrial inner membrane protein
Synonyms: OXA1Hs, OXA1-like protein, oxidase (cytochrome c) assembly 1-like, hsa, mitochondrial inner membrane protein OXA1L, oxidase assembly 1-like protein, OXA1L1, OXA1, MGC133129
Source: HGNC:8526
Biotype: protein coding gene
NDUFAB1
(Homo sapiens)Gene
Name: NADH:ubiquinone oxidoreductase subunit AB1
Synonyms: CI-SDAP, mitochondrial acyl carrier protein, complex I SDAP subunit, NADH-ubiquinone oxidoreductase 9.6 kDa subunit, SDAP, NADH:ubiquinone oxidoreductase SDAP subunit, acyl carrier protein, mitochondrial, FASN2A, ACP1, ACP, NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa, MGC65095
Source: HGNC:7694
Biotype: protein coding gene
MIEF1
(Homo sapiens)Gene
Name: mitochondrial elongation factor 1
Synonyms: SMCR7L, mitochondrial dynamic protein MID51, HSU79252, FLJ20232, mitochondrial dynamics protein of 51 kDa, MIEF1 upstream open reading frame protein, dJ1104E15.3, mitochondrial dynamics protein MID51, SMCR7-like protein, AL022312.1, MIEF1-MP, alternative protein SMCR7L, novel protein, Smith-Magenis syndrome chromosomal region candidate gene 7 protein-like, DANGER family member 3A, D3A, mitochondrial dynamic protein of 51 kDa, AltMIEF1, MIEF1 microprotein, mitochondrial dynamics protein MIEF1, MID51, Smith-Magenis syndrome chromosome region, candidate 7-like, OPA14, mitochondrial dynamics proteins of 51 kDa
Source: HGNC:25979
Biotype: protein coding gene
OXA1
(Saccharomyces cerevisiae)Gene
Name: cytochrome OXidase Activity
Synonyms: PET1402, YER154W
Source: SGD:S000000956
Biotype: protein coding gene
TMEM223
(Homo sapiens)Gene
Name: transmembrane protein 223
Synonyms: Mrx15, MGC3196
Source: HGNC:28464
Biotype: protein coding gene
GUF1
(Homo sapiens)Gene
Name: GTP binding elongation factor GUF1
Synonyms: GTP-binding protein GUF1 homolog, GUF1 GTPase homolog, GUF1 homolog, GTPase, EIEE40, ribosomal back-translocase, EF-4, GTPase GUF1, elongation factor 4 homolog, translation factor GUF1, mitochondrial, GTPase of unknown function 1, EF4, FLJ13220, DEE40
Source: HGNC:25799
Biotype: protein coding gene
C1qbp
(Mus musculus)Gene
Name: complement component 1, q subcomponent binding protein
Synonyms: AA986492, expressed sequence AA986492, D11Wsu182e, DNA segment, Chr 11, Wayne State University 182, expressed, gC1qR, AA407365, expressed sequence AA407365, P32, Habp1, HABP1
Source: MGI:1194505
Biotype: protein coding gene
GUF1
(Saccharomyces cerevisiae)Gene
Name: Gtpase of Unknown Function
Synonyms: YLR289W
Source: SGD:S000004280
Biotype: protein coding gene
METTL17
(Homo sapiens)Gene
Name: methyltransferase like 17
Synonyms: METT11D1, FLJ20859, methyltransferase-like protein 17, mitochondrial, methyltransferase 11 domain containing 1, ribosome assembly protein METTL17, mitochondrial, methyltransferase 11 domain-containing protein 1, false p73 target gene protein, protein RSM22 homolog, mitochondrial
Source: HGNC:19280
Biotype: protein coding gene
MRPS27
(Homo sapiens)Gene
Name: mitochondrial ribosomal protein S27
Synonyms: mitochondrial small ribosomal subunit protein mS27, mitochondrial 28S ribosomal protein S27, FLJ38645, S27mt, FLJ21764, FLJ23348, mS27, 28S ribosomal protein S27, mitochondrial, KIAA0264, MRP-S27, small ribosomal subunit protein mS27
Source: HGNC:14512
Biotype: protein coding gene
Taco1
(Mus musculus)Gene
Name: translational activator of mitochondrially encoded cytochrome c oxidase I
Synonyms: Ccdc44, RGD1306784, RIKEN cDNA 2310066I18 gene, 2310066I18Rik, coiled-coil domain containing 44
Source: MGI:1917457
Biotype: protein coding gene
MAM33
(Saccharomyces cerevisiae)Gene
Name: Mitochondrial Acidic Matrix protein
Synonyms: YIL070C
Source: SGD:S000001332
Biotype: protein coding gene
Guf1
(Mus musculus)Gene
Name: GUF1 homolog, GTPase
Synonyms: expressed sequence AA407526, AA407526, RGD1310774, mtEF4
Source: MGI:2140726
Biotype: protein coding gene
CG4882
(Drosophila melanogaster)Gene
Name: Not Available
Synonyms: anon-60Aa, UD1, GM14313, LD24471, undefined 1
Source: FB:FBgn0025336
Biotype: protein coding gene
Mrps27
(Mus musculus)Gene
Name: mitochondrial ribosomal protein S27
Synonyms: 2610028H14Rik, RIKEN cDNA 2610028H14 gene
Source: MGI:1919064
Biotype: protein coding gene
Ndufab1
(Mus musculus)Gene
Name: NADH:ubiquinone oxidoreductase subunit AB1
Synonyms: RIKEN cDNA 2610003B19 gene, RIKEN cDNA 2310039H15 gene, RIKEN cDNA 2210401F17 gene, RIKEN cDNA 9130423F15 gene, 9130423F15Rik, 8kDa, 2210401F17Rik, 2310039H15Rik, 2610003B19Rik
Source: MGI:1917566
Biotype: protein coding gene
C1qbp
(Rattus norvegicus)Gene
Name: complement C1q binding protein
Synonyms: glycoprotein gC1qBP, MGC91723, GC1q-R protein, complement component 1, q subcomponent binding protein, gC1qR, Habp1, complement component 1 Q subcomponent-binding protein, mitochondrial
Source: RGD:2230
Biotype: protein coding gene
CG4957
(Drosophila melanogaster)Gene
Name: Not Available
Synonyms: Not Available
Source: FB:FBgn0032205
Biotype: protein coding gene
Tmem223
(Mus musculus)Gene
Name: transmembrane protein 223
Synonyms: 0610006I08Rik, RIKEN cDNA 0610006I08 gene
Source: MGI:1914086
Biotype: protein coding gene
Uqcc5
(Mus musculus)Gene
Name: ubiquinol-cytochrome c reductase complex assembly factor 5
Synonyms: predicted gene, 41122, Gm41122, Smim4, RIKEN cDNA 2010107H07 gene, small integral membrane protein 4, 2010107H07Rik
Source: MGI:1913737
Biotype: protein coding gene
MRX15
(Saccharomyces cerevisiae)Gene
Name: Mitochondrial oRganization of gene eXpression (MIOREX)
Synonyms: YNR040W, DPI29
Source: SGD:S000005323
Biotype: protein coding gene
Mettl17
(Mus musculus)Gene
Name: methyltransferase like 17
Synonyms: 2310032K15Rik, RGD1559895, methyltransferase 11 domain containing 1, DNA segment, Chr 14, ERATO Doi 209, expressed, D14Ertd209e, RIKEN cDNA 2310032K15 gene, Mett11d1
Source: MGI:1098577
Biotype: protein coding gene
Ndufab1
(Rattus norvegicus)Gene
Name: NADH:ubiquinone oxidoreductase subunit AB1
Synonyms: LOC293453, acyl carrier protein, mitochondrial, NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1
Source: RGD:1305619
Biotype: protein coding gene
guf1
(Danio rerio)Gene
Name: GTP binding elongation factor GUF1
Synonyms: wu:fc88c11, im:6906935, fc88c11
Source: ZFIN:ZDB-GENE-030131-4289
Biotype: protein coding gene
Taco1
(Rattus norvegicus)Gene
Name: translational activator of cytochrome c oxidase I
Synonyms: similar to clone HQ0477 PRO0477p, Ccdc44, RGD1306784, LOC360645, coiled-coil domain-containing protein 44, translational activator of mitochondrially encoded cytochrome c oxidase I, translational activator of mitochondrially-encoded cytochrome c oxidase I, translational activator of cytochrome c oxidase 1, coiled-coil domain containing 44
Source: RGD:1306784
Biotype: protein coding gene
Mief1
(Rattus norvegicus)Gene
Name: mitochondrial elongation factor 1
Synonyms: mitochondrial dynamic protein MID51, MGC94326, Smith-Magenis syndrome chromosome region, candidate 7-like (human), mitochondrial dynamic protein of 51 kDa homolog, smith-Magenis syndrome chromosomal region candidate gene 7 protein-like, mitochondrial dynamics protein MID51, Smith-Magenis syndrome chromosome region, candidate 7-like, Smcr7l, hypothetical LOC315141, mitochondrial dynamics protein of 51 kDa homolog
Source: RGD:1359173
Biotype: protein coding gene
ZK1236.1
(Caenorhabditis elegans)Gene
Name: Translation factor GUF1 homolog, mitochondrial
Synonyms: CELE_ZK1236.1
Source: WB:WBGene00022862
Biotype: protein coding gene
waw
(Drosophila melanogaster)Gene
Name: waclaw
Synonyms: tu2, CG1410, CG32527, anon-19Fb
Source: FB:FBgn0024182
Biotype: protein coding gene
Mrps27
(Rattus norvegicus)Gene
Name: mitochondrial ribosomal protein S27
Synonyms: LOC361883, 28S ribosomal protein S27, mitochondrial, small ribosomal subunit protein mS27
Source: RGD:1311829
Biotype: protein coding gene
Oxa1l
(Rattus norvegicus)Gene
Name: OXA1L, mitochondrial inner membrane protein
Synonyms: LOC691393, oxidase (cytochrome c) assembly 1-like, mitochondrial inner membrane protein OXA1L, oxidase assembly 1-like, similar to Inner membrane protein OXA1L, mitochondrial precursor (Oxidase assembly 1-like protein) (OXA1-like protein)
Source: RGD:1585024
Biotype: protein coding gene
Malsu1
(Rattus norvegicus)Gene
Name: mitochondrial assembly of ribosomal large subunit 1
Synonyms: RGD1306936, uncharacterized protein LOC297082, similar to chromosome 7 open reading frame 30, LOC297082, mitochondrial assembly of ribosomal large subunit protein 1, hypothetical protein LOC297082
Source: RGD:1306936
Biotype: protein coding gene
Malsu1
(Mus musculus)Gene
Name: mitochondrial assembly of ribosomal large subunit 1
Synonyms: RGD1306936, RIKEN cDNA 2410003K15 gene, 2410003K15Rik
Source: MGI:1922843
Biotype: protein coding gene
LOC134479940
(Rattus norvegicus)Gene
Name: mitochondrial ribosome and complex I assembly factor AltMIEF1
Synonyms: Not Available
Source: RGD:402096099
Biotype: protein coding gene
Tmem223
(Rattus norvegicus)Gene
Name: transmembrane protein 223
Synonyms: similar to CG12935-PA, LOC690285
Source: RGD:1582829
Biotype: protein coding gene
Uqcc5
(Rattus norvegicus)Gene
Name: ubiquinol-cytochrome c reductase complex assembly factor 5
Synonyms: Smim4, small nucleolar RNA host gene (non-protein coding) 8, small integral membrane protein 4, LOC361111, Snhg8, RGD1307583
Source: RGD:1307583
Biotype: protein coding gene
MALSU1
(Homo sapiens)Gene
Name: mitochondrial assembly of ribosomal large subunit 1
Synonyms: C7orf30, mitochondrial assembly of ribosomal large subunit protein 1, mtRsfA, hypothetical protein LOC115416, uncharacterized protein C7orf30
Source: HGNC:21721
Biotype: protein coding gene
Ndufab1-ps
(Mus musculus)Gene
Name: NADH:ubiquinone oxidoreductase subunit AB1b
Synonyms: predicted gene, 17257, Gm17257
Source: MGI:4936891
Biotype: pseudogene
Oxa1l
(Mus musculus)Gene
Name: oxidase assembly 1-like
Synonyms: 1810020M02Rik, AI894287, expressed sequence AI894287, RIKEN cDNA 1810020M02 gene
Source: MGI:1916339
Biotype: protein coding gene
Mettl17
(Rattus norvegicus)Gene
Name: methyltransferase like 17
Synonyms: LOC305845, similar to FLJ20859 protein, methyltransferase-like protein 17, mitochondrial, RGD1559895, methyltransferase 11 domain containing 1, Mett11d1
Source: RGD:1559895
Biotype: protein coding gene
UQCC5
(Homo sapiens)Gene
Name: ubiquinol-cytochrome c reductase complex assembly factor 5
Synonyms: UPF0640 protein C3orf78, SMIM4, ubiquinol-cytochrome-c reductase complex assembly factor 5, small integral membrane protein 4, hypothetical protein LOC440957, small nucleolar rna host gene (non-protein coding) 8, C3orf78
Source: HGNC:37257
Biotype: protein coding gene
MDM38
(Saccharomyces cerevisiae)Gene
Name: Mitochondrial Distribution and Morphology
Synonyms: MKH1, YOL027C
Source: SGD:S000005387
Biotype: protein coding gene
AIM23
(Saccharomyces cerevisiae)Gene
Name: Altered Inheritance rate of Mitochondria
Synonyms: YJL131C, MIF3
Source: SGD:S000003667
Biotype: protein coding gene
Guf1
(Rattus norvegicus)Gene
Name: GTP binding elongation factor GUF1
Synonyms: GUF1 GTPase homolog, GTP-binding protein GUF1 homolog, GUF1 GTPase, GUF1 homolog, GTPase, LOC305317, RGD1310774, similar to expressed sequence AA407526 isoform a, translation factor GUF1, mitochondrial, GUF1 GTPase homolog (S. cerevisiae)
Source: RGD:1310774
Biotype: protein coding gene
tmem223
(Danio rerio)Gene
Name: transmembrane protein 223
Synonyms: zgc:101024
Source: ZFIN:ZDB-GENE-040801-113
Biotype: protein coding gene
MBA1
(Saccharomyces cerevisiae)Gene
Name: Multi-copy Bypass of AFG3
Synonyms: YBR185C
Source: SGD:S000000389
Biotype: protein coding gene